[Giant cell fibroblastoma associated with Darier-Ferrand dermatofibrosarcoma in an adult].
M. Kourda, H Krichen, H. Kennou, K. Ben Yahia, Mohamed Ben Ayed, Rafika Souissi
Abstract
M. Kourda, H Krichen, H. Kennou, K. Ben Yahia, Mohamed Ben Ayed, Rafika Souissi
Abstract
INTRODUCTION: Giant cell fibroblastoma is a rare mesenchyma tumor of childhood having many similarities with dermatofibrosarcoma protuberans in adults. OBSERVATION: We report the case of a 28-year-old woman presenting a subcutaneous inter-mammary mass associating both tumors. Immunohistochemistry showed an expression of CD 34 only by dermatofibrosarcoma protuberans cells. DISCUSSION: It is important to stress: the rarity of this association, the difficulty to confirm the diagnosis and to establish the links between these two tumors: simple association (as in our case), transformation or recurrence of giant cell fibroblastoma in dermatofibrosarcoma protuberans.
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INTRODUCTION: Giant cell fibroblastoma is a rare mesenchyma tumor of childhood having many similarities with dermatofibrosarcoma protuberans in adults. OBSERVATION: We report the case of a 28-year-old woman presenting a subcutaneous inter-mammary mass associating both tumors. Immunohistochemistry showed an expression of CD 34 only by dermatofibrosarcoma protuberans cells. DISCUSSION: It is important to stress: the rarity of this association, the difficulty to confirm the diagnosis and to establish the links between these two tumors: simple association (as in our case), transformation or recurrence of giant cell fibroblastoma in dermatofibrosarcoma protuberans.
Key concepts: Dermatofibrosarcoma protuberans, Dermatofibrosarcoma, Medicine, Pathology, Immunohistochemistry, Giant cell, Dermatology