CT characteristics of desmoplastic small round cell tumor:Six cases report and literatures review

Objective To investigate the CT characteristics of desmoplastic small round cell tumor (DSRCT) occurring in abdomen and pelvis. Methods Clinical data and CT images of 6 patients with DSRCT whose lesions occurring in abdomen and pelvis were retrospectively analyzed in combination with literature review. Results According to the CT manifestations,DSRCT could be divided into three types:①Peritoneal soft tissue mass (single or multiple,n=3),characteristiced with single or multiple tumors in the peritoneal cavity,inhomogeneity,with calcification; ②Diffuse irregular peritoneal thickening type,without any distinguishable peritoneal masses (n=1); ③Soft tissue mass originated from organs of the abdomen (pelvis) or retroperitoneal,irregular mass,inhomogeneity with punctate or patchy calcification (n=2). Conclusion CT manifestations of the DSRCT occurring in the abdomen and pelvis are variety,and are indistinguishable from other diseases.