The Expected Contribution of the Domestic Intramedullary Telescopic System to the Surgical Treatment of Children with Osteogenesis Imperfecta in Kazakhstan

Osteogenesis imperfecta (OI) is a group of inherited connective tissue disorders in collagen structure, processing or cross-linking, new bone formation and osteoblast differentiation, which result in fragility of the bones, recurrent fractures and deformities.The article presents scientific data on the types and features of metal structures used in intramedullary osteotomy performed for the surgical treatment of fractures and deformities of long tubular bones with osteogenesis imperfecta in children and outlines the benefits of the developed domestic intramedullary telescopic system "DOSSANOV" in providing surgical treatment to children with osteogenesis imperfecta. For the "crystal children", whose number is growing in Kazakhstan, the expected advantages of using this system are analyzed.Key words: Osteogenesis imperfecta, children, intramedullary osteosynthesis, osteotomy, intramedullary rods, intramedullary telescopic system.