Neonatal pyloric stenosis in the early neonatal period

Background : Neonatal hypertrophic pyloric stenosis is a rare pathological entity in pediatrics. The incidence of hypertrophic pyloric stenosis is 1-3 per 1000 live births in the neonatal period. Case Presentation: We have presented a 4-day-old male who has non-projectile, non-bilious vomiting and has not passed stool for the last two days. Necessary investigations have been carried out, and the final diagnosis was made by an ultrasound of the abdomen, which revealed hypertrophic pyloric stenosis. Ramstedt's Pyloromyotomy was performed to correct pyloric stenosis alongside intraoperative findings of malrotation of the gut with normal mesentery and small gut. Conclusion: In this report, we have discussed the presentation of, hypertrophic pyloric stenosis in the early neonatal period with no electrolyte imbalance, no metabolic alkalosis ( varies from usual presentation ) and associated malrotation of the gut. In Pakistan, hypertrophic pyloric stenosis in the early neonatal period has not been documented before.