Numerous anomalies of teeth with concomitant nonsyndromic oligodontia in primary and permanent dentition: A rare case report

Aim: The case report aimed at reporting a rare case of numerous morphological anomalies of teeth with concomitant nonsyndromic oligodontia in primary and permanent dentition in the oral cavity. Background: Oligodontia is agenesis of numerous teeth preferably missing more than six teeth in the oral cavity, affects both primary and permanent dentition, and is commonly associated with ectodermal dysplasia or specific abnormalities. Agenesis of the primary teeth is rare, especially of the primary canines. The exact etiology is unknown. Case description: This paper reports a very rare case of an 8-year-old boy with multiple morphological anomalies of teeth, with missing primary canines, and 19 permanent teeth at 8 years of age, later followed up from 11 to 15 years. This paper discusses the prevalence, etiology, and management of oligodontia which was not associated with any syndrome like Van Der Woude, Reiger syndrome as it usually is, because the patient did not exhibit any of the associated findings with any syndrome, thereby making it rare of the rare cases. Conclusion: A rare case report of nonsyndromic oligodontia with multiple congenitally missing primary and permanent teeth associated with morphological anomalies of the teeth and without the absence of any systemic disorders or syndromes is presented. Clinical Significance: Since oligodontia is always associated with ectodermal dysplasia or other syndromes, recognizing cases without associated syndromes which are necessary to evaluate any other underlying factors. Thus, the incidence of oligodontia which usually varies from 0.08% to 0.16% citing this case report falls into that 1% making it rare.