Progression of liver fibrosis in a type 2 biliary atresia female baby before hepatoportoenterostomy

Abstract Type 2 biliary atresia is a relatively rare type of biliary atresia, and it is sometimes difficult to differentiate it from choledochal cysts. This report describes a female newborn with prenatal diagnosis of choledochal cyst who had intermittent clay color stool after birth. The transient elastography showed progressive liver stiffness before surgery, and the intraoperative cholangiogram confirmed the diagnosis of type 2 cystic type biliary atresia. The baby then received hepatoportoenterostomy, and the liver stiffness also declined smoothly after the operation.