2018•Journal of Cystic FibrosisOpen access

IVACAFTOR restores FGF19 regulated bile acid homeostasis in cystic fibrosis patients with an S1251N or a G551D gating mutation

Ivo P. van de Peppel, Marcela Doktorova, Gitte Berkers, Hugo R. de Jonge, Roderick H.J. Houwen, Henkjan J. Verkade, Johan W. Jonker, Frank A.J.A. Bodewes

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Key concepts: Ivacaftor, FGF19, Enterohepatic circulation, Cystic fibrosis, Cystic fibrosis transmembrane conductance regulator, Medicine, Internal medicine, Bile acid