Symptomatic Fetal-Type Cardiac Rhabdomyoma.
Şeyma Kayalı, Vehbi Doğan, Nilüfer Arda, Murat Koç, İlker Ertuğrul, Senem Özgür, Utku Arman Örün, Selmin Karademir
Abstract
Şeyma Kayalı, Vehbi Doğan, Nilüfer Arda, Murat Koç, İlker Ertuğrul, Senem Özgür, Utku Arman Örün, Selmin Karademir
Abstract
Rhabdomyomas are the most common primary cardiac tumors, especially seen during early periods of childhood. Fetaltype rhabdomyoma is a benign tumor described almost always in extracardiac locations. Although the natural history of the cardiac rhabdomyoma is to regress, the behaviour of the fetal-type rhabdomyomas when present in the heart is unknown with respect to its infrequency. Herein, we report a hemodynamically unstable female neonate with a single large intra-cardiac mass unresponsive to medical treatment, who underwent surgery. The neonate could not survive the operation due to ventricular fibrillation. The mass was diagnosed as fetal-type cardiac rhabdomyoma on autopsy.
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Rhabdomyomas are the most common primary cardiac tumors, especially seen during early periods of childhood. Fetaltype rhabdomyoma is a benign tumor described almost always in extracardiac locations. Although the natural history of the cardiac rhabdomyoma is to regress, the behaviour of the fetal-type rhabdomyomas when present in the heart is unknown with respect to its infrequency. Herein, we report a hemodynamically unstable female neonate with a single large intra-cardiac mass unresponsive to medical treatment, who underwent surgery. The neonate could not survive the operation due to ventricular fibrillation. The mass was diagnosed as fetal-type cardiac rhabdomyoma on autopsy.
Key concepts: Rhabdomyoma, Medicine, Autopsy, Fetus, Cardiology, Cardiac surgery, Internal medicine, Cardiac Tumors