Repercussões clínicas e radiológicas do neurofibroma plexiforme na região pélvica* Clinical and radiological repercussions of plexiform neurofibroma in the pelvic region

Slaibi EB, Daher JGL, Fonseca GGG, Daher CM, Geller M, Ribeiro MG. Repercussoes clinicas e radiologicas do neurofibroma plexifo rme na regiao pelvica.Radiol Bras. 2014 Set/Out;47(5):326–328.ResumoAbstractDescricao de caso de neurofibroma plexiforme localizado na regiao pelvica comprometendo bexiga, prostata e coluna lombossacra, comevolucao de tres anos e seis meses. Diante de contraindicacao de remocao cirurgica, foi realizado acompanhamento clinico e radi ologicosemestral, sem constatacao de crescimento tumoral. Na neurofibromatose tipo 1, as manifestacoes clinicas sao diversas e a equip emedica deve estar atenta a investigacao complementar e pode ser surpreendida por um achado raro. As massas pelvicas volumosaspodem, eventualmente, corresponder a neurofibromas plexiformes, sendo util a investigacao de neurofibromatose caso o pacienteainda nao tenha esse diagnostico.Unitermos: Neurofibromatose tipo 1; Neurofibroma plexiforme; Pelve.The authors report the case of a plexiform neurofibroma located in the pelvis, affecting the bladder, prostate and spine (lumba r/sacral),followed-up for three years and six months. Surgical removal was contraindicated and the patient underwent biannual clinical an d radiologicalfollow-up that did not demonstrate any tumor increase. The clinical manifestations of neurofibromatosis type 1 are variable, an d themedical team should be attentive to further investigations, considering possible unexpected rare findings. Large pelvic masses may correspondto plexiform neurofibromas, so the diagnostic hypothesis of neurofibromatosis should be taken into consideration.Keywords: Neurofibromatosis type 1; Plexiform neurofibroma; Pelvis.