A case report of dextrocardia with incomplete visceral heterotaxy

Heterotaxy means different arrangement, these grouped into bilateral right sidedness or right isomerism and bilateral left sidedness or left isomerism. Normally there is asymmetric arrangement of thoracic, cardiac and abdominal organs. When there is symmetry asplenia or polysplenia syndromes results with complex congenital heart disease. Asplenia has bad prognosis in early neonatal period. The morbidity and mortality of polysplenia is associated with complex cardiac lesion. This case is a five year old boy with presented with recurrent respiratory tract infection and clinically dextrocardia with evidence of left to right shunt. Investigation revealed atrial situs inversus with AV, VA concordance with systemic and pulmonary venous anomalies and left pulmonary vein stenosis, bronchial situs ambiguous with right side IVC and aorta without life threatening cardiac and extracardiac anomalies.