1979•PubMedRequires access
[Congenital cystic dilatation of the intrahepatic bile ducts. Caroli's disease and its complications].
U Seefeld, Melanie Jaeger, A Akovbiantz, Martina Maranta, Fritz Heinzel, M. Schmid
Open publisher page 2 citations
Abstract
Two cases with congenital dilatations of the intrahepatic bile ducts are reported. The clinical, diagnostic and therapeutic aspects and possible complications of this rare disease are discussed. The well-known frequent occurrence of cholangiocarcinoma in Caroli's disease is illustrated by one of our patients. Because of the limited therapeutic possibilities, the prognosis of this illness remains unfavourable.