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[Primary leiomyosarcoma of bone: a clinico-pathologic and immunohistochemical study of 3 cases].

Dominique Wendum, Alain Sautet, S. Prévot, D. Martel, A Apoil, P. P. de Saint Maur

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Abstract

Primary leiomyosarcoma of bone is rare. Herein we describe 3 cases with immunohistochemical study. All 3 cases were positive for smooth muscle actin and/or desmin. None was positive for cytokeratin. Differential diagnosis includes metastatic spindle cell carcinoma, other sarcoma (fibrosarcoma, malignant fibrous histiocytoma) and metastatic extra-osseous leiomyosarcoma, mostly from uterus or digestive tract.

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What this paper is about

Primary leiomyosarcoma of bone is rare. Herein we describe 3 cases with immunohistochemical study. All 3 cases were positive for smooth muscle actin and/or desmin. None was positive for cytokeratin. Differential diagnosis includes metastatic spindle cell carcinoma, other sarcoma (fibrosarcoma, malignant fibrous histiocytoma) and metastatic extra-osseous leiomyosarcoma, mostly from uterus or digestive tract.

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Available abstract

Primary leiomyosarcoma of bone is rare. Herein we describe 3 cases with immunohistochemical study. All 3 cases were positive for smooth muscle actin and/or desmin. None was positive for cytokeratin. Differential diagnosis includes metastatic spindle cell carcinoma, other sarcoma (fibrosarcoma, malignant fibrous histiocytoma) and metastatic extra-osseous leiomyosarcoma, mostly from uterus or digestive tract.

Key concepts: Desmin, Leiomyosarcoma, Immunohistochemistry, Fibrosarcoma, Cytokeratin, Pathology, Sarcoma, Differential diagnosis

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[Primary leiomyosarcoma of bone: a clinico-pathologic and immunohistochemical study of 3 cases]. — Research Paper | ScholarLens