Appearance of high resolution CT in congenital inner ear malformations

Objective:To discuss the high resolution CT(HRCT) appearance of the congenital inner ear malformations.Methods:The HRCT appearance of 29 cases(46 ears) with congenital inner ear malformations were analyzed retrospectively.The axial images and multi-planar reconstruction were performed in each patient,and the 3D reconstruction of inner ear labrinth were done with volume rendering technique.Results:Seventeen patients were bilateral inner ear malformations among 29 patients.There are 46 ears with inner ear malformations.The malformations were(1)Michel deformity(2 ear),(2)cochlear aplasia(6 ears),(3)common cavity deformity(5 ears),(4)incomplete partitionⅠ(5 ears),(5)incomplete partition Ⅱ(traditional Mondini deformity)(17 ears),(6)vestibular and/or semicircular canal malformaitions(9 ears),(7)internal auditory canal malformations(2 ears).Conclusion:HRCT is very useful to the diagnosis of the cingenital inner ear malformations,and can provide an important evidence for the cochlear implantation.