Ultrasound in diagnosis of autosomal recessive polycystic kidney disease complicated with congenital hepatic fibrosis

Objective To observe the value of ultrasound in diagnosis of autosomal recessive polycystic kidney disease(ARPKD) complicated with congenital hepatic fibrosis(CHF).Methods The clinical and ultrasonic data of 7patients with ARPKD were retrospectively analyzed.Results The kidneys of 7cases manifested as increased volume,inhomogeneous echo of renal parenchyma with diffuse spot hyperecho and loss of the normal corticomedullary distinction.Using high frequency ultrasound,numerous microcysts were observed,and part or all the cortex and medulla were involved.The livers enlarged in 6cases,and mild dilated and stiff intrahepatic bile duct and enhanced periportal echo were observed.Cystic dilation of bile duct was found in 1case at right posterior lobe of the liver.Conclusion Ultrasound plays an important role in diagnosis of ARPKD complicated with CHF.High frequency ultrasound is helpful to displaying the characteristic changes of kidney in patients with ARPKD.