Sudden death in a patient with idiopathic right ventricular outflow tract arrhythmia

Idiopathic ventricular tachycardia originating from the right ventricular outflow tract (RVOT) and idiopathic RVOT extrasystoles are generally considered benign arrhythmias. We describe the case of a patient with typical RVOT arrhythmias without any symptoms for many years, who died suddenly the day before a planned electrophysiological study. The only disquieting signs in her clinical history were a relatively short coupling interval of premature ventricular contractions in some ECG recordings and an isolated run of polymorphic nonsustained ventricular tachycardia induced by an RVOT extrasystole during previous ECG monitoring.