Osteogenesis Imperfecta/Lobstein Syndrome associated with Dentinogenesis Imperfecta
Naresh Lingaraju, Nagarathna PJ, Devaki Vijayalakshmi, P Sheshadri
Abstract
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Naresh Lingaraju, Nagarathna PJ, Devaki Vijayalakshmi, P Sheshadri
Abstract
Open-access reader
ABSTRACT Osteogenesis imperfecta is a collagen related disorder characterized by increased bone fragility and low bone mass. The important oral finding in osteogenesis imperfect is the presence of dentinogenesis imperfecta. This article presents a case of osteogenesis imperfecta (type IV B) with dentinogenesis imperfecta where a 7-year-old girl had opalacent primary teeth associated with severe bone deformity, scoliosis, barrel shaped rib cage, and short stature. The clinical, radiographic ad histologic features are reviewed along with management aspects. How to cite this article Lingaraju N, Nagarathna PJ, Vijayalakshmi R, Sheshadri P. Osteogenesis Imperfecta/ Lobstein Syndrome associated with Dentinogenesis Imperfecta. J Contemp Dent Pract 2013;14(1):140-142.
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ABSTRACT Osteogenesis imperfecta is a collagen related disorder characterized by increased bone fragility and low bone mass. The important oral finding in osteogenesis imperfect is the presence of dentinogenesis imperfecta. This article presents a case of osteogenesis imperfecta (type IV B) with dentinogenesis imperfecta where a 7-year-old girl had opalacent primary teeth associated with severe bone deformity, scoliosis, barrel shaped rib cage, and short stature. The clinical, radiographic ad histologic features are reviewed along with management aspects. How to cite this article Lingaraju N, Nagarathna PJ, Vijayalakshmi R, Sheshadri P. Osteogenesis Imperfecta/ Lobstein Syndrome associated with Dentinogenesis Imperfecta. J Contemp Dent Pract 2013;14(1):140-142.
Key concepts: Dentinogenesis imperfecta, Osteogenesis imperfecta, Medicine, Short stature, Deformity, Dentistry, Scoliosis, Orthodontics