Transfusion Therapy in a Patient With Erythropoietic Protoporphyria
Mark A. Bechtel
Abstract
Mark A. Bechtel
Abstract
An 8-year-old boy with erythropoietic protoporphyria had a marked decrease in photosensitivity symptoms after several transfusions with washed, packed RBCs. The reduction in photosensitivity was associated with a decline in free erythrocyte protoporphyrin levels.
OpenAlex reports 34 citations for this work. Citation counts describe recorded attention and do not establish research quality.
A contribution statement is not available in the OpenAlex record.
Method details are not available in the OpenAlex metadata.
Findings are not separately available in the OpenAlex metadata.
Limitations are not available in the OpenAlex metadata.
Application details are not available in the OpenAlex metadata.
An 8-year-old boy with erythropoietic protoporphyria had a marked decrease in photosensitivity symptoms after several transfusions with washed, packed RBCs. The reduction in photosensitivity was associated with a decline in free erythrocyte protoporphyrin levels.
Key concepts: Erythropoietic protoporphyria, Photosensitivity, Medicine, Protoporphyrin, Dermatology, Porphyria, Surgery, Porphyrin