CT of CNS lesions in lymphomatoid granulomatosis: case report.

Neurologic manifestations of lymphomatoid granulomatosis occur in 20-30% of cases. The disease is primarily an unusual form of pulmonary angiitis, and was first described in 1972 by Liebow et al. [1] . The purpose of this paper is to show the progression and regression of CNS lesions in a 17-year-old boy who presented only with neurologic features of the disease. Patients with lymphomatoid granulomatosis are usually quite ill with pulmonary manifestations. In our study, lymphomatoid granulomatosis initially manifested purely as a CNS disease that was later followed by histologically proved abdominal involvement and radiologic evidence of chest involvement.