Angiokeratoma circumscriptum in a child of Klippel-Trenaunay syndrome: A rare association

Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterized by capillary malformation, vascular anomalies, and bony and soft tissue hypertrophy. Angiokeratomas are of several types. Angiokeratoma circumscriptum (AC) is a nevoid form which presents as dark red papules and plaques mostly with a verrucous surface. AC is itself very rare. KTS along with AC is even rarer. Here, we present a rare case of KTS with AC on the background of port-wine stain.