SJÖGREN'S SYNDROME IN ASSOCIATION WITH SCLERODERMA

Case Reports1 June 1960SJÖGREN'S SYNDROME IN ASSOCIATION WITH SCLERODERMAMARTIN A. SHEARN, M.D.MARTIN A. SHEARN, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-52-6-1352 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptThe symptom complex known as the sicca syndrome, or Sjögren's syndrome, has been observed frequently in conjunction with rheumatoid arthritis. A relationship between this syndrome and the other diseases that affect primarily connective tissues has been suggested but rarely documented. The purpose of the present paper is to report the association of the sicca syndrome with scleroderma in two patients, and to review the literature relating this syndrome to collagen diseases.In a series of contributions beginning in 1933, expanding previous observations, Sjögren1helped to establish a symptom complex that has become known as the sicca syndrome, or Sjögren's syndrome....Bibliography1. Sjögren H: Zur Kenntnis der Keratoconjunctivitis sicca, Acta ophth. (Suppl. 2) 11: 1, 1933. Google Scholar2. Forster HW: Rose bengal test in diagnosis of deficient tear formation, Arch. Ophth. 45: 419, 1951. CrossrefMedlineGoogle Scholar3. Sjögren H: Keratoconjunctivitis sicca and the sicca syndrome, some actual problems, Tr. Ophth. Soc. Australia 11: 27, 1951. Google Scholar4. Holm S: Keratoconjunctivitis sicca and the sicca syndrome, Acta ophth. (Suppl. 33) 27: 1, 1949. Google Scholar5. Houwer AW: Keratitis filamentosa and chronic arthritis, Tr. Ophth. Soc. U. Kingdom 47: 88, 1927. 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Path. and Bact. 68: 137, 1954. CrossrefMedlineGoogle Scholar20. McLeanRobinson KHS: Sjögren's syndrome, Canad. M. A. J. 71: 597, 1954. MedlineGoogle Scholar21. Heaton JM: Sjögren's syndrome and systemic lupus erythematosus, Brit. M. J. 1: 466, 1959. CrossrefMedlineGoogle Scholar22. Morgan WS: The probable systemic nature of Mikulicz's disease and its relation to Sjögren's syndrome, New England J. Med. 251: 5, 1954. CrossrefMedlineGoogle Scholar23. CaugheyRichardson JEW: Acrosclerosis; with a report of a case treated with cortisone, New Zealand M. J. 51: 227, 1952. MedlineGoogle Scholar24. Kaposi M: Neue Beiträge zur Kenntnis des Lupus erythematosus, Arch. Dermat. u. Syph. 4: 36, 1872. CrossrefGoogle Scholar25. ShearnPirofsky MAB: Disseminated lupus erythematosus: analysis of 34 cases, Arch. Int. Med. 90: 790, 1952. CrossrefGoogle Scholar26. Shearn MA: Unpublished cases. Google Scholar27. HarveySchulmanTumultyConleySchoenrich AMLEPACLEH: Systemic lupus erythematosus: review of the literature and clinical analysis of 138 cases, Medicine 33: 291, 1954. CrossrefMedlineGoogle Scholar28. MorganCastleman WSB: Clinicopathologic study of Mikulicz's disease, Am. J. Path. 29: 471, 1953. MedlineGoogle Scholar29. SeifertGeiler GG: Salivary glands and rheumatic disease, German M. Month. 3: 87, 1958. Google Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Oakland, California*Received for publication December 17, 1958.From the Department of Medicine, Permanente Medical Group, Kaiser Foundation Hospital, Oakland, California.Requests for reprints should be addressed to Martin A. Shearn, M.D., Director of Medical Education, Kaiser Foundation Hospital, 280 West MacArthur Boulevard, Oakland 11, California. 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FRANKLIN, M.D., DONALD F. HILL, M.D., F.A.C.P., JOSEPH LEE HOLLANDER, M.D., F.A.C.P., HOWARD L. HOLLEY, M.D., F.A.C.P., JOHN G. MAYNE, M.D., F.A.C.P., WILLIAM M. MIKKELSEN, M.D., F.A.C.P., MAX M. MONTGOMERY, M.D., F.A.C.P., CARL M. PEARSON, M.D., F.A.C.P., CHARLES L. SHORT, M.D., F.A.C.P., HUGH A. SMYTHE, M.D., F.R.C.P. (C), OTTO STEINBROCKER, M.D.Sjögren's syndrome and its relation to connective tissue diseasesA review of recent observations and current theories on the etiology and pathogenesis of progressive systemic sclerosis (diffuse scleroderma)A Clinical Study of Sjögren's SyndromeNEAL A. VANSELOW, M.D., VERNON N. DODSON, M.D., DAVID C. ANGELL, M.D., IVAN F. DUFF, M.D., F.A.C.P.Familial Occurrence of Collagen Diseases: I. Progressive Systemic Sclerosis and Systemic Lupus Erythematosus 1 June 1960Volume 52, Issue 6Page: 1352-1362KeywordsArthritisCollagen diseasesConnective tissue diseasesCorneaHospital medicineMucous membranesRheumatoid arthritisSclerodermaVagina ePublished: 1 December 2008 Issue Published: 1 June 1960 PDF downloadLoading ...